2024-03-28T14:50:58Z
https://u-ryukyu.repo.nii.ac.jp/oai
oai:u-ryukyu.repo.nii.ac.jp:02016476
2022-02-22T06:14:43Z
1642838163960:1642838198944:1642838242961:1642838252330
1642838403551:1642838412624
[原著]先天性第11因子欠乏症を伴った大動脈弁閉鎖不全症の1例
Successful Aortic Valve Replacement in a Patient with Congenital Factor 11 Deficiency
池村, 冨士夫
伊波, 潔
国吉, 幸男
上里, 忠興
喜名, 盛夫
屋良, 勲
古謝, 景春
Ikemura, Fujio
Iha, Kiyoshi
Kuniyoshi, Yukio
Uezato, Tadaoki
Kina, Morio
Yara, Isao
Kojya, Kageharu
Aortic valve replacement with SJM mechanical valve was successfully performed in a 23-year-old male with congenital factor 11 deficiency (hemophilia c). Aortic valve insufficiency was confirmed by cardiac catheterization and aortography. Specific assay for factor 11 using plasma artificially depleted of factor 11 was done, and his factor 11 plasma level was only 3 %. Preoperatively, he received fresh forzen plasma, so that factor 11 level rised to 56 %, and open heart surgery was performed safely. To our knowledge, the patient described is the first patient with congentital factor 11 deficiency to undergo valve replacement in the world.
論文
http://purl.org/coar/resource_type/c_6501
琉球大学医学部
Faculty of Medicine, University of the Ryukyus
VoR
0285-9270
AN00250763
琉球大学保健学医学雑誌=Ryukyu University Journal of Health Sciences and Medicine
3
5
245
241
jpn
open access
琉球医学会