{"created":"2022-02-01T06:35:31.223261+00:00","id":2011135,"links":{},"metadata":{"_buckets":{"deposit":"47d660c5-ab90-42ba-9a00-bde2a022f71c"},"_deposit":{"id":"2011135","owners":[1],"pid":{"revision_id":0,"type":"depid","value":"2011135"},"status":"published"},"_oai":{"id":"oai:u-ryukyu.repo.nii.ac.jp:02011135","sets":["1642838163960:1642838338003","1642838403551:1642838407795"]},"author_link":[],"item_1617186331708":{"attribute_name":"Title","attribute_value_mlt":[{"subitem_title":"IPNA clinical practice recommendations for the diagnosis and management of children with steroid-resistant nephrotic syndrome","subitem_title_language":"en"}]},"item_1617186419668":{"attribute_name":"Creator","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"Trautmann, Agnes","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Vivarelli, Marina","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Samuel, Susan","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Gipson, Debbie","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Sinha, Aditi","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Schaefer, Franz","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Hui, Ng Kar","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Boyer, Olivia","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Saleem, Moin A","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Feltran, Luciana","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Müller-Deile, Janina","creatorNameLang":"ja"}]},{"creatorNames":[{"creatorName":"Becker, Jan Ulrich","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Cano, Francisco","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Xu, Hong","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Lim, Yam Ngo","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Smoyer, William","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Anochie, Ifeoma","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Nakanishi, Koichi","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Hodson, Elisabeth","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Haffner, Dieter","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"International Pediatric Nephrology Association","creatorNameLang":"en"}]}]},"item_1617186476635":{"attribute_name":"Access Rights","attribute_value_mlt":[{"subitem_access_right":"open access","subitem_access_right_uri":"http://purl.org/coar/access_right/c_abf2"}]},"item_1617186609386":{"attribute_name":"Subject","attribute_value_mlt":[{"subitem_subject":"Steroid-resistant nephrotic syndrome","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Children","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Chronic kidney disease","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Genetics","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Outcome","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Pediatrics","subitem_subject_language":"en","subitem_subject_scheme":"Other"},{"subitem_subject":"Immunosuppressive treatment","subitem_subject_language":"en","subitem_subject_scheme":"Other"}]},"item_1617186626617":{"attribute_name":"Description","attribute_value_mlt":[{"subitem_description":"Idiopathic nephrotic syndrome newly affects 1–3 per 100,000 children per year. Approximately 85% of cases show complete remission of proteinuria following glucocorticoid treatment. Patients who do not achieve complete remission within 4–6 weeks of glucocorticoid treatment have steroid-resistant nephrotic syndrome (SRNS). In 10–30% of steroid-resistant patients, mutations in podocyte-associated genes can be detected, whereas an undefined circulating factor of immune origin is assumed in the remaining ones. Diagnosis and management of SRNS is a great challenge due to its heterogeneous etiology, frequent lack of remission by further immunosuppressive treatment, and severe complications including the development of end-stage kidney disease and recurrence after renal transplantation. A team of experts including pediatric nephrologists and renal geneticists from the International Pediatric Nephrology Association (IPNA), a renal pathologist, and an adult nephrologist have now developed comprehensive clinical practice recommendations on the diagnosis and management of SRNS in children. The team performed a systematic literature review on 9 clinically relevant PICO (Patient or Population covered, Intervention, Comparator, Outcome) questions, formulated recommendations and formally graded them at a consensus meeting, with input from patient representatives and a dietician acting as external advisors and a voting panel of pediatric nephrologists. Research recommendations are also given.","subitem_description_type":"Other"},{"subitem_description":"論文","subitem_description_type":"Other"}]},"item_1617186643794":{"attribute_name":"Publisher","attribute_value_mlt":[{"subitem_publisher":"Springer","subitem_publisher_language":"en"}]},"item_1617186702042":{"attribute_name":"Language","attribute_value_mlt":[{"subitem_language":"eng"}]},"item_1617186783814":{"attribute_name":"Identifier","attribute_value_mlt":[{"subitem_identifier_type":"HDL","subitem_identifier_uri":"http://hdl.handle.net/20.500.12000/46947"}]},"item_1617186920753":{"attribute_name":"Source Identifier","attribute_value_mlt":[{"subitem_source_identifier":"0931-041X","subitem_source_identifier_type":"ISSN"},{"subitem_source_identifier":"1432-198X","subitem_source_identifier_type":"ISSN"}]},"item_1617186941041":{"attribute_name":"Source Title","attribute_value_mlt":[{"subitem_source_title":"Pediatric Nephrology","subitem_source_title_language":"en"}]},"item_1617187056579":{"attribute_name":"Bibliographic Information","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2020-05-07","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"8","bibliographicPageEnd":"1561","bibliographicPageStart":"1529","bibliographicVolumeNumber":"35"}]},"item_1617258105262":{"attribute_name":"Resource Type","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_1617265215918":{"attribute_name":"Version Type","attribute_value_mlt":[{"subitem_version_resource":"http://purl.org/coar/version/c_970fb48d4fbd8a85","subitem_version_type":"VoR"}]},"item_1617353299429":{"attribute_name":"Relation","attribute_value_mlt":[{"subitem_relation_type_id":{"subitem_relation_type_id_text":"https://doi.org/10.1007/s00467-020-04519-1","subitem_relation_type_select":"DOI"}},{"subitem_relation_type_id":{"subitem_relation_type_id_text":"https://doi.org/10.1007/s00467-020-04519-1","subitem_relation_type_select":"DOI"}}]},"item_1617605131499":{"attribute_name":"File","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_access","filename":"Trautmann2020_Article_IPNAClinicalPracticeRecommenda.pdf","mimetype":"application/pdf","url":{"objectType":"fulltext","url":"https://u-ryukyu.repo.nii.ac.jp/record/2011135/files/Trautmann2020_Article_IPNAClinicalPracticeRecommenda.pdf"},"version_id":"1e4cc754-7f00-4d9a-b8f4-0375575f0047"}]},"item_title":"IPNA clinical practice recommendations for the diagnosis and management of children with steroid-resistant nephrotic syndrome","item_type_id":"15","owner":"1","path":["1642838338003","1642838407795"],"pubdate":{"attribute_name":"PubDate","attribute_value":"2020-10-12"},"publish_date":"2020-10-12","publish_status":"0","recid":"2011135","relation_version_is_last":true,"title":["IPNA clinical practice recommendations for the diagnosis and management of children with steroid-resistant nephrotic syndrome"],"weko_creator_id":"1","weko_shared_id":-1},"updated":"2023-08-03T05:35:00.762913+00:00"}