@article{oai:u-ryukyu.repo.nii.ac.jp:02011152, author = {Nitta, Hayase and Taira, Yusuke and Kinjo, Tadatsugu and Chinen, Yukiko and Masamoto, Hitoshi and Sanabe, Naoya and Goya, Hideki and Yoshida, Tomohide and Sugibayashi, Rika and Sumie, Masahiro and Wada, Seiji and Sago, Haruhiko and Aoki, Yoichi}, issue = {3}, journal = {American Journal of Perinatology Reports}, month = {Jul}, note = {Aim We report a case of congenital pulmonary airway malformation (CPAM) with hydrops in which the fetus underwent thoracoamniotic shunting.\nCase Report A 40-year-old (G1P1) woman was diagnosed with a macrocystic CPAM. Thoracoamniotic shunting was performed at 19 weeks of gestation but not well drained and was successfully performed again at 23 weeks. However, the CPAM volume ratio, abdominal circumference, and amniotic fluid index started increasing from 28 weeks and hydrops worsened. The insufficient shunting and the fetal cardiac failure had to be considered. At 32 weeks, a male infant with general edema and massive ascites was born weighing 3,362 g (+4.79 SD) with Apgar scores of 2 and 4. The infant was intubated and high-frequency oscillation and nitric oxide therapies were instituted. The resection of CPAM was performed on day 2. Nasal continuous positive airway pressure was instituted on day 16. The infant was discharged and prescribed with home oxygen therapy (HOT) on day 65. The infant was able to leave the HOT at 30 months and is currently 34 months of age in good condition.\nConclusion Fetal thoracoamniotic shunting may be life-saving in CPAM complicated by hydrops and that this treatment might be sufficient to cure the child., 論文}, pages = {e185--e187}, title = {Fetal Thoracoamniotic Shunting in a Case of Congenital Pulmonary Airway Malformations with Hydrops Fetalis}, volume = {7}, year = {2017} }