{"created":"2022-02-22T03:01:52.083623+00:00","id":2015607,"links":{},"metadata":{"_buckets":{"deposit":"2dad951e-d97f-41f4-94be-1302311d522f"},"_deposit":{"id":"2015607","owners":[1],"pid":{"revision_id":0,"type":"depid","value":"2015607"},"status":"published"},"_oai":{"id":"oai:u-ryukyu.repo.nii.ac.jp:02015607","sets":["1642838163960:1642838198944:1642838199408:1642838222821","1642838403551:1642838412624"]},"author_link":[],"item_1617186331708":{"attribute_name":"Title","attribute_value_mlt":[{"subitem_1551255647225":"［症例報告］Pulmonary Hypoplasia and Chondrocyte p21^<CIP1> Expression in Patients with Lethal Short-limbed Dwarfism","subitem_1551255648112":"ja"}]},"item_1617186419668":{"attribute_name":"Creator","attribute_type":"creator","attribute_value_mlt":[{"creatorNames":[{"creatorName":"Suzuiu, Masumi","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Tanaka, Takuji","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Mori, Hideki","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Nakayama, Takashi","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Aonahata, Miyuki","creatorNameLang":"en"}]},{"creatorNames":[{"creatorName":"Yoshimi, Naoki","creatorNameLang":"en"}]}]},"item_1617186476635":{"attribute_name":"Access Rights","attribute_value_mlt":[{"subitem_1522299639480":"open access","subitem_1600958577026":"http://purl.org/coar/access_right/c_abf2"}]},"item_1617186499011":{"attribute_name":"Rights","attribute_value_mlt":[{"subitem_1522650717957":"ja","subitem_1522651041219":"琉球医学会"}]},"item_1617186609386":{"attribute_name":"Subject","attribute_value_mlt":[{"subitem_1522299896455":"en","subitem_1522300014469":"Other","subitem_1523261968819":"short-limbed dwarfism"},{"subitem_1522299896455":"en","subitem_1522300014469":"Other","subitem_1523261968819":"pulmonary hypoplasia"},{"subitem_1522299896455":"en","subitem_1522300014469":"Other","subitem_1523261968819":"p21^<CIPI1>"},{"subitem_1522299896455":"en","subitem_1522300014469":"Other","subitem_1523261968819":"thanatophoric dysplasia"},{"subitem_1522299896455":"en","subitem_1522300014469":"Other","subitem_1523261968819":"hypophosphatasia"}]},"item_1617186626617":{"attribute_name":"Description","attribute_value_mlt":[{"subitem_description":"Lethal short-limbed dwarfism is a rare disorder associated with chondrodysplasia, micromeha, and severe pulmonary hypoplasia. Thus, most of the affected infants are stillborn or die shortly because of respiratory insufficiency. Two autopsy cases of lethal short-limbed drawfism are presented in this article. Both stillborn infants had markedly short extremities and small thorax. Pulmonary alveolar cells were immature and air apace was diminished. Chondrocytes of a long bone showed hypertrophy and irregular arrangement. Growth plate chondrocytes displayed a significant expression of the p21^<CIP1> protein. This is the systematic examination of the autopsy cases that highlight pulmonary hypoplasia and chondrocyte p21^CIPI1 expression in patients with lethal short-limbed dwarfism.","subitem_description_type":"Other"},{"subitem_description":"論文","subitem_description_type":"Other"}]},"item_1617186643794":{"attribute_name":"Publisher","attribute_value_mlt":[{"subitem_1522300295150":"ja","subitem_1522300316516":"琉球医学会"},{"subitem_1522300295150":"en","subitem_1522300316516":"Ryukyu Medical Association"}]},"item_1617186702042":{"attribute_name":"Language","attribute_value_mlt":[{"subitem_1551255818386":"eng"}]},"item_1617186920753":{"attribute_name":"Source Identifier","attribute_value_mlt":[{"subitem_1522646500366":"ISSN","subitem_1522646572813":"1346-888X"},{"subitem_1522646500366":"ISSN","subitem_1522646572813":"0289-1530"},{"subitem_1522646500366":"NCID","subitem_1522646572813":"AN10369445"}]},"item_1617186941041":{"attribute_name":"Source Title","attribute_value_mlt":[{"subitem_1522650068558":"ja","subitem_1522650091861":"琉球医学会誌 = Ryukyu Medical Journal"}]},"item_1617187056579":{"attribute_name":"Bibliographic Information","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"2006","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"1・2","bibliographicPageEnd":"46","bibliographicPageStart":"41","bibliographicVolumeNumber":"25"}]},"item_1617258105262":{"attribute_name":"Resource Type","attribute_value_mlt":[{"resourcetype":"journal article","resourceuri":"http://purl.org/coar/resource_type/c_6501"}]},"item_1617265215918":{"attribute_name":"Version Type","attribute_value_mlt":[{"subitem_1522305645492":"VoR","subitem_1600292170262":"http://purl.org/coar/version/c_970fb48d4fbd8a85"}]},"item_1617605131499":{"attribute_name":"File","attribute_type":"file","attribute_value_mlt":[{"accessrole":"open_access","filename":"v25p41.pdf","mimetype":"application/pdf","url":{"objectType":"fulltext","url":"https://u-ryukyu.repo.nii.ac.jp/record/2015607/files/v25p41.pdf"},"version_id":"fb59077b-ec0a-4d1d-9202-a09c7f4daf37"}]},"item_title":"［症例報告］Pulmonary Hypoplasia and Chondrocyte p21^<CIP1> Expression in Patients with Lethal Short-limbed Dwarfism","item_type_id":"15","owner":"1","path":["1642838222821","1642838412624"],"pubdate":{"attribute_name":"PubDate","attribute_value":"2010-02-23"},"publish_date":"2010-02-23","publish_status":"0","recid":"2015607","relation_version_is_last":true,"title":["［症例報告］Pulmonary Hypoplasia and Chondrocyte p21^<CIP1> Expression in Patients with Lethal Short-limbed Dwarfism"],"weko_creator_id":"1","weko_shared_id":-1},"updated":"2022-10-31T07:41:02.760086+00:00"}