@article{oai:u-ryukyu.repo.nii.ac.jp:02016476, author = {池村, 冨士夫 and 伊波, 潔 and 国吉, 幸男 and 上里, 忠興 and 喜名, 盛夫 and 屋良, 勲 and 古謝, 景春 and Ikemura, Fujio and Iha, Kiyoshi and Kuniyoshi, Yukio and Uezato, Tadaoki and Kina, Morio and Yara, Isao and Kojya, Kageharu}, issue = {3}, journal = {琉球大学保健学医学雑誌=Ryukyu University Journal of Health Sciences and Medicine}, note = {Aortic valve replacement with SJM mechanical valve was successfully performed in a 23-year-old male with congenital factor 11 deficiency (hemophilia c). Aortic valve insufficiency was confirmed by cardiac catheterization and aortography. Specific assay for factor 11 using plasma artificially depleted of factor 11 was done, and his factor 11 plasma level was only 3 %. Preoperatively, he received fresh forzen plasma, so that factor 11 level rised to 56 %, and open heart surgery was performed safely. To our knowledge, the patient described is the first patient with congentital factor 11 deficiency to undergo valve replacement in the world., 論文}, pages = {241--245}, title = {[原著]先天性第11因子欠乏症を伴った大動脈弁閉鎖不全症の1例}, volume = {5} }