{"_buckets": {"deposit": "47d660c5-ab90-42ba-9a00-bde2a022f71c"}, "_deposit": {"id": "2011135", "owners": [1], "pid": {"revision_id": 0, "type": "depid", "value": "2011135"}, "status": "published"}, "_oai": {"id": "oai:u-ryukyu.repo.nii.ac.jp:02011135", "sets": ["1642838338003", "1642838407795"]}, "author_link": [], "item_1617186331708": {"attribute_name": "Title", "attribute_value_mlt": [{"subitem_1551255647225": "IPNA clinical practice recommendations for the diagnosis and management of children with steroid-resistant nephrotic syndrome", "subitem_1551255648112": "en"}]}, "item_1617186419668": {"attribute_name": "Creator", "attribute_type": "creator", "attribute_value_mlt": [{"creatorNames": [{"creatorName": "Trautmann, Agnes", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Vivarelli, Marina", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Samuel, Susan", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Gipson, Debbie", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Sinha, Aditi", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Schaefer, Franz", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Hui, Ng Kar", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Boyer, Olivia", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Saleem, Moin A", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Feltran, Luciana", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Müller-Deile, Janina", "creatorNameLang": "ja"}]}, {"creatorNames": [{"creatorName": "Becker, Jan Ulrich", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Cano, Francisco", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Xu, Hong", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Lim, Yam Ngo", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Smoyer, William", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Anochie, Ifeoma", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Nakanishi, Koichi", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Hodson, Elisabeth", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "Haffner, Dieter", "creatorNameLang": "en"}]}, {"creatorNames": [{"creatorName": "International Pediatric Nephrology Association", "creatorNameLang": "en"}]}]}, "item_1617186476635": {"attribute_name": "Access Rights", "attribute_value_mlt": [{"subitem_1522299639480": "open access", "subitem_1600958577026": "http://purl.org/coar/access_right/c_abf2"}]}, "item_1617186609386": {"attribute_name": "Subject", "attribute_value_mlt": [{"subitem_1522299896455": "en", "subitem_1522300014469": "Other", "subitem_1523261968819": "Steroid-resistant nephrotic syndrome"}, {"subitem_1522299896455": "en", "subitem_1522300014469": "Other", "subitem_1523261968819": "Children"}, {"subitem_1522299896455": "en", "subitem_1522300014469": "Other", "subitem_1523261968819": "Chronic kidney disease"}, {"subitem_1522299896455": "en", "subitem_1522300014469": "Other", "subitem_1523261968819": "Genetics"}, {"subitem_1522299896455": "en", "subitem_1522300014469": "Other", "subitem_1523261968819": "Outcome"}, {"subitem_1522299896455": "en", "subitem_1522300014469": "Other", "subitem_1523261968819": "Pediatrics"}, {"subitem_1522299896455": "en", "subitem_1522300014469": "Other", "subitem_1523261968819": "Immunosuppressive treatment"}]}, "item_1617186626617": {"attribute_name": "Description", "attribute_value_mlt": [{"subitem_description": "Idiopathic nephrotic syndrome newly affects 1–3 per 100,000 children per year. Approximately 85% of cases show complete remission of proteinuria following glucocorticoid treatment. Patients who do not achieve complete remission within 4–6 weeks of glucocorticoid treatment have steroid-resistant nephrotic syndrome (SRNS). In 10–30% of steroid-resistant patients, mutations in podocyte-associated genes can be detected, whereas an undefined circulating factor of immune origin is assumed in the remaining ones. Diagnosis and management of SRNS is a great challenge due to its heterogeneous etiology, frequent lack of remission by further immunosuppressive treatment, and severe complications including the development of end-stage kidney disease and recurrence after renal transplantation. A team of experts including pediatric nephrologists and renal geneticists from the International Pediatric Nephrology Association (IPNA), a renal pathologist, and an adult nephrologist have now developed comprehensive clinical practice recommendations on the diagnosis and management of SRNS in children. The team performed a systematic literature review on 9 clinically relevant PICO (Patient or Population covered, Intervention, Comparator, Outcome) questions, formulated recommendations and formally graded them at a consensus meeting, with input from patient representatives and a dietician acting as external advisors and a voting panel of pediatric nephrologists. Research recommendations are also given.", "subitem_description_type": "Other"}, {"subitem_description": "論文", "subitem_description_type": "Other"}]}, "item_1617186643794": {"attribute_name": "Publisher", "attribute_value_mlt": [{"subitem_1522300295150": "en", "subitem_1522300316516": "Springer"}]}, "item_1617186702042": {"attribute_name": "Language", "attribute_value_mlt": [{"subitem_1551255818386": "eng"}]}, "item_1617186783814": {"attribute_name": "Identifier", "attribute_value_mlt": [{"subitem_identifier_type": "HDL", "subitem_identifier_uri": "http://hdl.handle.net/20.500.12000/46947"}]}, "item_1617186920753": {"attribute_name": "Source Identifier", "attribute_value_mlt": [{"subitem_1522646500366": "ISSN", "subitem_1522646572813": "0931-041X"}, {"subitem_1522646500366": "ISSN", "subitem_1522646572813": "1432-198X"}]}, "item_1617186941041": {"attribute_name": "Source Title", "attribute_value_mlt": [{"subitem_1522650068558": "en", "subitem_1522650091861": "Pediatric Nephrology"}]}, "item_1617187056579": {"attribute_name": "Bibliographic Information", "attribute_value_mlt": [{"bibliographicIssueDates": {"bibliographicIssueDate": "2020-05-07", "bibliographicIssueDateType": "Issued"}, "bibliographicIssueNumber": "8", "bibliographicPageEnd": "1561", "bibliographicPageStart": "1529", "bibliographicVolumeNumber": "35"}]}, "item_1617258105262": {"attribute_name": "Resource Type", "attribute_value_mlt": [{"resourcetype": "journal article", "resourceuri": "http://purl.org/coar/resource_type/c_6501"}]}, "item_1617265215918": {"attribute_name": "Version Type", "attribute_value_mlt": [{"subitem_1522305645492": "VoR", "subitem_1600292170262": "http://purl.org/coar/version/c_970fb48d4fbd8a85"}]}, "item_1617353299429": {"attribute_name": "Relation", "attribute_value_mlt": [{"subitem_1522306287251": {"subitem_1522306382014": "DOI", "subitem_1522306436033": "https://doi.org/10.1007/s00467-020-04519-1"}}, {"subitem_1522306287251": {"subitem_1522306382014": "DOI", "subitem_1522306436033": "https://doi.org/10.1007/s00467-020-04519-1"}}]}, "item_1617605131499": {"attribute_name": "File", "attribute_type": "file", "attribute_value_mlt": [{"accessrole": "open_access", "download_preview_message": "", "file_order": 0, "filename": "Trautmann2020_Article_IPNAClinicalPracticeRecommenda.pdf", "future_date_message": "", "is_thumbnail": false, "mimetype": "", "size": 0, "url": {"objectType": "fulltext", "url": "https://u-ryukyu.repo.nii.ac.jp/record/2011135/files/Trautmann2020_Article_IPNAClinicalPracticeRecommenda.pdf"}, "version_id": "1e4cc754-7f00-4d9a-b8f4-0375575f0047"}]}, "item_title": "IPNA clinical practice recommendations for the diagnosis and management of children with steroid-resistant nephrotic syndrome", "item_type_id": "15", "owner": "1", "path": ["1642838338003", "1642838407795"], "permalink_uri": "http://hdl.handle.net/20.500.12000/46947", "pubdate": {"attribute_name": "PubDate", "attribute_value": "2020-10-12"}, "publish_date": "2020-10-12", "publish_status": "0", "recid": "2011135", "relation": {}, "relation_version_is_last": true, "title": ["IPNA clinical practice recommendations for the diagnosis and management of children with steroid-resistant nephrotic syndrome"], "weko_shared_id": -1}
IPNA clinical practice recommendations for the diagnosis and management of children with steroid-resistant nephrotic syndrome
http://hdl.handle.net/20.500.12000/46947
http://hdl.handle.net/20.500.12000/46947