Item type |
デフォルトアイテムタイプ(フル)(1) |
公開日 |
2010-07-02 |
タイトル |
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タイトル |
[症例報告]原発性胆汁性肝硬変を合併した皮膚筋炎の1例 |
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言語 |
ja |
タイトル |
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タイトル |
Dermatomyositis Associated with Primary Biliary Cirrhosis |
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言語 |
en |
作成者 |
秋坂, 真史
安達, 正則
鈴木, 信
諸喜田, 林
佐久川, 廣
斎藤, 厚
Akisaka, Masafumi
Adachi, Masanori
Suzuki, Makoto
Shokita, Hayashi
Sakugawa, Hiroshi
Saito, Atsushi
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アクセス権 |
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アクセス権 |
open access |
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アクセス権URI |
http://purl.org/coar/access_right/c_abf2 |
権利情報 |
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言語 |
ja |
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権利情報 |
琉球医学会 |
主題 |
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言語 |
en |
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主題Scheme |
Other |
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主題 |
dermatomyositis |
主題 |
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言語 |
en |
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主題Scheme |
Other |
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主題 |
primary biliary cirrhosis |
主題 |
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言語 |
en |
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主題Scheme |
Other |
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主題 |
pulmonary fibrosis |
内容記述 |
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内容記述タイプ |
Other |
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内容記述 |
A 66-year-old woman was admitted to our hospital because of exacerbation of dermatomyositis. She had been treated as dermatomyositis since 1986. She also suffered from liver cirrhosis of unknown etiology and diabetes mellitus. She complained of fever, muscle weakness and myalgia in proximal extremities. Physical examination disclosed body temperature of 37℃, a sealy erythema on her forehead, purpuric rash of the eyelids, cyanosis, clubbing of the fingers and toes. Symmetrical atrophies in proximal limb muscle were evident and museles were tender to palpation. Auscultation of the heart revealed a midsystolic murmur in apex. Dry rales were heard in bilateral bases of the lung. Abdominal palpation showed a hepatosplenomegaly. Laboratory findings include erythrocyte sedimentation rate 100 mm/h, serum phosphokinase 326 U/L, serum GOT 98 IU/L, serum LDH 718 IU/L, serum total bilirubin 2.2 mg/dl, serum myoglobin 84 ng/dl. Antimitochondrial antibody was positive. The electromyogram study was normal but the muscle biopsy showed slight myopathic change. The liver biopsy demonstrated lymphocytes infiltration, destruction of limiting membranes, which were compatible with Primary Bilialy Cirrhosis(PBC). The final diagnosis of her illness ineluded 1) dermatomyositis, 2) PBC, 3) pulmonary fibrosis and 4) diabetes mellitus. Clinical manifestations gradually improved with predonisolone therapy. However, because of hypoxia and congestive heart failure, rehabilitation for muscle weakness could not be done sufficiently. Dermatomyositis associated with PBC is very rare, although 21 patients with polymyositis associated with PBC were reported to our best knowledge. |
内容記述 |
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内容記述タイプ |
Other |
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内容記述 |
論文 |
出版者 |
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言語 |
ja |
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出版者 |
琉球医学会 |
出版者 |
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言語 |
en |
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出版者 |
Ryukyu Medical Association |
言語 |
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言語 |
jpn |
資源タイプ |
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資源タイプ |
journal article |
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資源タイプ識別子 |
http://purl.org/coar/resource_type/c_6501 |
出版タイプ |
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出版タイプ |
VoR |
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出版タイプResource |
http://purl.org/coar/version/c_970fb48d4fbd8a85 |
収録物識別子 |
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収録物識別子タイプ |
ISSN |
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収録物識別子 |
1346888X |
収録物識別子 |
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収録物識別子タイプ |
ISSN |
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収録物識別子 |
0289-1530 |
収録物識別子 |
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収録物識別子タイプ |
NCID |
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収録物識別子 |
AN10369445 |
収録物名 |
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言語 |
ja |
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収録物名 |
琉球医学会誌 = Ryukyu Medical Journal |
書誌情報 |
巻 13,
号 1,
p. 63-69,
発行日 1993
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